Thursday, November 02, 2006

Allgrove Syndrome

Allgrove Syndrome

General:  Autosomal dominant

Ocular: Distichiasis, conjuncitivits, keratitis, congenital alacrima

Clinical: ACTH insensitivitiy, achialasia

Moore PS, Couch RM, Perry YS, et.al.:  Allgrove syndrome: An autosomal recessive syndrome of ACTH insensitivity, achialasia and alacrima.  Clin Endocrimal. 1991; 34: 107-114.

Davidoff E, Friedman AH: Congenital alacrima.  Surv Ophthalmol 1997; 22: 113-118.  

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